Systemic primary amyloidosis in chronic hemodialysis
نویسنده
چکیده
A patient with end-stage renal disease undergoing chronic hemodialysis presented with disseminated systemic primary amyloidosis without evidence of ?2microglobulin deposition. Multiorgan involvement proved by biopsy was present in breast, lymph nodes, gastric mucosa, and bone marrow. Imaging studies and biochemical testing revealed evidence suggesting involvement of other organ systems, including thyroid, heart, liver, and adrenal gland. It is emphasized that amyloidosis may present with myriad clinical features. Appropriate subclassification of amyloid protein is imperative for defining intervention and treatment.
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تاریخ انتشار 2011